John D. Chovan, James R. Cacchillo
Nursing, Congenital heart defects
Medical Pathology | Nursing
Congenital heart defects requiring single ventricle palliation are a rare but life-threatening occurrence. There are multiple defects resulting in single ventricle physiology including defects in which the right or left ventricle within the heart is either undeveloped (hypoplastic left heart syndrome, hypoplastic right heart syndrome), or the valve to the main pulmonary artery did not form (pulmonary atresia). These defects prevent the heart from supplying adequate blood flow to the lungs or body. Single ventricle congenital heart defects are not easily treated surgically due to their complexity in nature. Single ventricle surgical palliation typically involves three open-heart surgeries including the Norwood or Hybrid Procedure, the Bidirectional Glenn procedure, and finally the Fontan procedure, (Hardiman, 2013, p. 327).
Dunkleberger, Alaina, "Protein Losing Enteropathy following Fontan Palliation in the Single Ventricle Population" (2014). Master of Science in Nursing (MSN) Student Scholarship. Paper 1.